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Anti-HOGA1抗體,HOGA1蛋白抗體品牌直供產(chǎn)品介紹:DHDPSL is a 327 amino acid mitochondrial protein that catalyzes the last step in the hydroxyproline metabolic pathway. Existing as two alternatively spliced isoforms, DHDPSL is expressed in kidney and liver and is inhibited by divalent cations. Defects in the gene that encode DHDPSL are the cause of primary hyperoxalurea type III (HP3), a disorder of calcium oxalate nephrolithiasis. Patients with HP3 excrete urine with elevated levels of oxalate and L-glycerate. The DHDPSL gene maps to human chromosome 10, which contains over 800 genes and 135 million nucleotides. Defects in some of the genes that map to chromosome 10 are associated with Charcot-Marie Tooth disease, Jackson-Weiss syndrome, Usher syndrome, nonsyndromatic deafness, Wolman’s syndrome, Cowden syndrome, multiple endocrine neoplasia type 2 and porphyria.
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保存條件:Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
連續(xù)使用時4°C存儲,保質(zhì)期六個月,*存儲時建議分裝為10ul以上小包裝-20°C存儲,并避免反復(fù)凍融,保質(zhì)期一年。
產(chǎn)品名稱 Anti-HOGA1抗體,HOGA1蛋白抗體品牌直供
產(chǎn)品編號 BYK-17348R
英文名稱 HOGA1
中文名稱 HOGA1蛋白抗體
別 名 4 hydroxy 2 oxoglutarate aldolase 1; C10orf65; DHDPS like protein; DHDPS2; DHDPSL; Dihydrodipicolinate synthase like; Dihydrodipicolinate synthase like, mitochondrial; Dihydrodipicolinate synthetase homolog 2; FLJ37472; HOGA1; HOGA1_HUMAN; HP3; mitochondrial; N acetylneuraminate pyruvate lyase 2 (putative); NPL2; Probable 2 keto 4 hydroxyglutarate aldolase; Probable 4 hydroxy 2 oxoglutarate aldolase mitochondrial; Probable 4-hydroxy-2-oxoglutarate aldolase; Probable KHG aldolase; Protein 569272.
研究領(lǐng)域 細(xì)胞生物 信號轉(zhuǎn)導(dǎo) 新陳代謝
抗體來源 Rabbit or Mouse
克隆類型 Polyclonal or Monoclonal
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Anti-HOGA1抗體,HOGA1蛋白抗體品牌直供更多優(yōu)質(zhì)產(chǎn)品有:
信號轉(zhuǎn)導(dǎo)和轉(zhuǎn)錄激活因子5抗體 Anti-STAT5
RhoB蛋白抗體 Anti-Rho B
信號轉(zhuǎn)導(dǎo)和轉(zhuǎn)錄激活因子4抗體 Anti-STAT4
釉基質(zhì)蛋白抗體 Anti-AMBN
信號轉(zhuǎn)導(dǎo)和轉(zhuǎn)錄激活因子3抗體 Anti-STAT3
原鈣粘蛋白γA1抗體 Anti-PCDHGA1
磷酸化信號轉(zhuǎn)導(dǎo)和轉(zhuǎn)錄激活因子6抗體 Anti-phospho-STAT6(Tyr641)
眼部白化病相關(guān)蛋白OA1/蛋白偶聯(lián)受體143抗體 Anti-OA1/GPR143
磷酸化信號轉(zhuǎn)導(dǎo)和轉(zhuǎn)錄激活因子5a抗體 Anti-phospho-STAT5a(Tyr694)
GRC5蛋白抗體 Anti-GRC5/PHF2
磷酸化信號轉(zhuǎn)導(dǎo)和轉(zhuǎn)錄激活因子3抗體 Anti-phospho-STAT3 (Tyr705)
乙酰*結(jié)合蛋白抗體 Anti-ACBD
前列腺跨膜上皮1抗原抗體 Anti-STEAP1
環(huán)一螺旋蛋白1抗體 Anti-NHLH1
信號轉(zhuǎn)導(dǎo)和轉(zhuǎn)錄激活因子2抗體 Anti-STAT2
原鈣粘蛋白β7抗體 Anti-PCDHB7
磷酸化信號轉(zhuǎn)導(dǎo)與轉(zhuǎn)錄激活因子1抗體 Anti-phospho-STAT1(Tyr701)
視神經(jīng)細(xì)胞相關(guān)蛋白/早老素結(jié)合蛋白抗體 Anti-DOCK3
信號轉(zhuǎn)導(dǎo)與轉(zhuǎn)錄激活因子1抗體 Anti-STAT1
*或半*蛋白水解酶抑制蛋白1抗體 Anti-Neuroserpin
*受體4抗體 Anti-SSTR4
核因子1X抗體 Anti-NFIX
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